Abstract. Background: Hypertrophic pachymeningitis is an uncommon disorder that causes a localized or diffuse thickening of the dura mater and has been. Summary: Idiopathic hypertrophic cranial pachymeningitis is a rare inflammatory disease with diffused involvement of the dura. Often, the definite diagnosis is. Hypertrophic pachymeningitis is a unique clinical entity characterised by fibrosis and thickening of the duramater with resulting neurological dysfunction.

Author: Fenrizil JoJotaur
Country: Singapore
Language: English (Spanish)
Genre: Relationship
Published (Last): 20 February 2017
Pages: 54
PDF File Size: 18.55 Mb
ePub File Size: 7.52 Mb
ISBN: 937-2-31616-327-4
Downloads: 88682
Price: Free* [*Free Regsitration Required]
Uploader: Mezisho

Cahill DW, Saleman M: Presence of associated leptomeningeal enhancement or parenchymal abnormalities with the exception of brain edema should suggest an alternate diagnosis.

National Center for Biotechnology InformationU. Introduction Hypertrophic pachymeningitis is a rare form of diffuse inflammatory disease that causes thickening of the dura mater.

Long term improvement of idiopathic hypertrophic cranial pachymeningitis by lymphocytapheresis. P-ANCA positive Wegener’s granulomatosis presenting with hypertrophic pachymeningitis and multiple cranial neuropathies: Presse Med ; MR imaging revealed diffuse dural enhancement and thickening, along with left fronto parieto occipital edema. A case of posterior fossa hypertrophic pachymeningitis with hydrocephalus. Aspecific headache during 13 years as the only symptom of idiopathic hypertrophic pachymeningitis.

Articles Cases Courses Quiz. Fungal and AFB culture were negative. It was first described by Charcot and later by Naffziger and Stern. Idiopathic hypertrophic cranial pachymeningitis: Two patients received surgical intervention.


How to cite this URL: To quiz yourself on this article, log pachymeningigis to see multiple choice questions.

Hypertrophic pachymeningitis

Connective tissue diseases and the nervous system. All patients were treated with corticosteroid and improved intially, but half of them experienced relapses. It is a fibrosing inflammatory process that involves the dura mater.

Tuberculous hypertrophic pachymeningitis involving the posterior fossa and high cervical region. Pathological examination in hyppertrophic autopsied cases revealed diffuse thickening of the dura, especially in the posterior part of the falx cerebri and the tentorium cerebelli.

A pchymeningitis lady presented with headache and progressive painless loss of vision in both the eyes over a periods of 6 months.

Recurrent cranial neuropathy as a clinical presentation of hypfrtrophic inflammation of the duramater: CT or MR imaging studies should be obtained to identify mass lesions in the brain stem or skull base. About Blog Go ad-free.

Many patients had mild to moderate elevation of C-reactive protein, and three patients had perinuclear antineutrophil cytoplasmic antibody. Footnotes Source of Support: Neurol Med Chir ; Report of three cases. Hypertrophic cranial pachymeningitis involving the pituitary gland: The CSF in most cases showed inflammatory changes. Churchill livingstone ; New York. Non-enhanced CT scans show thickened, hyperdense dura, typically along the tentorium, tentorial ridge, falx, and prepontine brain stem with marked enhancement on contrast administration.

Discussion Hypertrophic pachymeningitis is a rare disorder of diverse etiology.


Clin Exp Neurol ; One case had necrotizing vasculitis of the small arteries located in the dura and the cerebral surface. Loading Stack – 0 images remaining. Nil Conflict of Interest: Neuroimaging studies revealed diffuse or localized thickening of the dura, and MRI findings were key to diagnosis of this hypertroophic.

Dural masses dural masses meningioma grading and histological pacchymeningitis grade I meningothelial meningioma fibrous meningioma microcystic meningioma psammomatous meningioma angiomatous meningioma secretory meningioma metaplastic meningioma cartilaginous meningioma lipomatous meningioma melanotic meningioma myxoid meningioma osseous meningioma xanthomatous meningioma lymphoplasmacyte-rich meningioma grade II clear cell meningioma chordoid meningioma atypical meningioma grade III rhabdoid meningioma papillary meningioma anaplastic meningioma a.

This is an open-access article distributed under the terms of the Creative Commons Attribution-Noncommercial-Share Alike 3. There were no giant cells, caseation necrosis, or epitheloid granuloma. No Shinkei Geka ; The cell infiltration was marked at the surface of the dura mater. Varied manifestations of a single disease entity. The clinical course was chronic.

Hypertrophic pachymeningitis

Erdheim Chester disease Erdheim Chester disease. Check for errors and try again. Imaging appearance of pachymeningeal tuberculosis. Case 2 Case 2.